- Title
- Sclerosing paraganglioma of the carotid body in a child: A diagnostic and therapeutic challenge
- Creator
- Blefari, Nicholas D. A.; Eliezer, Dilharan D.; Vilain, Ricardo E.; Hesketh, Elizabeth E.; Deshpande, Arvind; Deshpande, Aniruddh V.
- Relation
- Internatioanl Journal of Pediatric Otorhinolaryngology Case Reports Vol. 23, Issue January 2019, no. 100663
- Publisher Link
- http://dx.doi.org/10.1016/j.pedeo.2019.100663
- Publisher
- Elsevier
- Resource Type
- journal article
- Date
- 2019
- Description
- Objectives: Carotid body tumours are rare in children, and a sclerosing carotid body paraganglioma has never been reported in the paediatric age group. We report a case of a young female with a sclerosing paraganglioma of the right carotid bifurcation and the unique management issues that it created. Methods & results: A nine-year-old girl presented with a painless, solid, right-sided cervical mass, which was encasing the bifurcation of the right common carotid artery. At operation, en-bloc resection of the carotid bifurcation was mandated because of difficult dissection between the tumour and the arterial wall. The external carotid artery stump was oversewn, and a saphenous vein interposition graft was used to reconstruct the common carotid to internal carotid arteries. Final pathology revealed a paraganglioma accompanied with dense stromal sclerosis, consistent with a sclerosing paraganglioma. Conclusion: The diagnosis of a sclerosing carotid body paraganglioma and its treatment in a child is challenging due to its rarity and histological features. We recommend a multidisciplinary approach to such a diagnosis, and plan for the possibility of arterial reconstruction.
- Subject
- sclerosing paraganglioma; carotid body tumour; paediatric tumour; carotid reconstruction; saphenous vein graft
- Identifier
- http://hdl.handle.net/1959.13/1509122
- Identifier
- uon:56209
- Identifier
- ISSN:2588-9109
- Language
- eng
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